High Tracheal Bifurcation as a Cause of Left Main Bronchus Obstruction in Infant: A case report from Saudi Arabia

M, Gawahir; A M, Khalid; E, Safa; A, Wadha

doi:10.21608/ejhm.2018.9119

High Tracheal Bifurcation as a Cause of Left Main Bronchus Obstruction in Infant: A case report from Saudi Arabia

Document Type : Original Article

Authors

¹ Pediatric Pulmonary division, King Fahad Medical City (KFMC)

² Pediatric Pulmonary Division, King Khalid Hospital/ King Saud University

³ Pediatric Pulmonary division, King Fahad Medical City(KFMC)

⁴ Pediatric Pulmonary and Sleep Physician, Head of the Pulmonary Unit, KFMC, KSA

10.21608/ejhm.2018.9119

Abstract

Background: Congenital short trachea (CST) an uncommon abnormality is defined as a reduction in the number of tracheal rings to 15 or less, compared to the average of 17 rings in normal infants. As a result, the carina is situated at a higher level than usual that lead the left main bronchus to course abnormally behind the arch of the aorta, making it prone to compression. CST is associated with a number of syndromes, including the Di George syndrome, several types of congenital heart disease, some skeletal dysplasias and meningomyelocoele. Case study: We report a case of one Saudi infant who presented with respiratory distress since birth and hyperinflation of left side of the lung secondary to extrinsic narrowing of proximal left main stem bronchus due to compression by arch of the aorta, and he underwent successful aortopexy of the aortic arch for this condition.

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